Neurorretinite estrelada idiopática de Leber: relato de caso em adolescente

Leber’s idiopathic stellate neuroretinitis: case report in adolescent

Authors

  • Leila Maas Pediatra e Médica de Adolescentes do Ambulatório do Núcleo de Estudos da Saúde do Adolescente – NESA/ UERJ. Rio de Janeiro, RJ, Brasil
  • Márcia Takey Pediatra e Médica de Adolescentes do Ambulatório do Núcleo de Estudos da Saúde do Adolescente – NESA/ UERJ. Rio de Janeiro, RJ, Brasil.
  • Tais Estrela Médica Residente de Oftalmologia da Universidade do Estado do Rio de Janeiro (UERJ). Rio de Janeiro, RJ, Brasil
  • Maria Teresa Silveira Médica responsável pelo Setor de Uveítes e AIDS da Disciplina de Oftalmologia do Hospital Universitário Pedro Ernesto (HUPE/UERJ). Rio de Janeiro, RJ, Brasil.

Keywords:

Adolescent, blindness, optic nerve.

Abstract

Objective: Evaluate a case of Leber’s idiopathic stellate neuroretinitis, a rare disease of ocular involvement in adolescent
admitted to our clinic unit. Case description: A 16-year old adolescent, the bearer of defi ciency of glucose 6-phosphate
dehydrogenase, with decrease of unilateral visual acuity, painless and progressive two months ago, optical disc edema and
peripapillary and macular star by funduscopic examination. given the negative fi ndings of laboratory tests, radiological
and serology the diagnosis of exclusion was Leber’s idiopathic stellate neuroretinitis. Comments: Leber’s idiopathic stellate
neuroretinitis (LiSN) is a clinical entity of diffi cult diagnosis. Several treatable diseases may have similar appearance to the
classic LiSN, and the accurate diagnosis may result in appropriate treatment and visual rehabilitation.

Published

2013-08-22

How to Cite

Maas, L., Takey, M., Estrela, T., & Teresa Silveira, M. (2013). Neurorretinite estrelada idiopática de Leber: relato de caso em adolescente: Leber’s idiopathic stellate neuroretinitis: case report in adolescent. Adolescência E Saúde, 10(4), 71–75. Retrieved from https://adolescenciaesaude.com/index.php/aes/article/view/458

Issue

Section

Original Articles